Fumarylacetoacetate

[HOOCCH=CHCOCH2COCH2COOH;an intermediate in phenylalanine and tyrosine catabolism; elevated in tyrosinaemia IA. fumarylacetoacetate hydrolase, an enzyme that catalyses the hydrolysis of fumarylacetoacetate to fumarate and acetoacetate; a deficiency indicates tyrosinaemia IA.

Molecular Formula: C₈H₆O₆^-2

InChI: InChI=1/C8H8O6/c9-5(1-2-7(11)12)3-6(10)4-8(13)14/h1-2H,3-4H2,(H,11,12)(H,13,14)/p-2/b2-1+/fC8H6O6/q-2

InChIKey: InChIKey=GACSIVHAIFQKTC-CGTUZVIRDS
SMILES: C(C(=O)CC(=O)[O-])C(=O)C=CC(=O)[O-]

Names:
    CHEBI:18034
    Fumarylacetoacetate
    (E)-4,6-dioxooct-2-enedioate
    (2E)-4,6-dioxooct-2-enedioate
    4-fumarylacetoacetate(2-)
    4-Fumarylacetoacetate

Registries:
    PubChem CID 5459934
    PubChem ID 8143913